Imperforate Ebstein's malformation in atrioventricular septal defect

Jeong-Wook Seo, Woo Hee Jung, Yong Won Park

Research output: Contribution to journalArticleResearchpeer-review

3 Citations (Scopus)

Abstract

Anatomic data are presented of a female abortus with the unusual combination of Ebstein's malformation and atrioventricular septal defect with right isomerism of the atrial appendages, left-hand ventricular topology and discordant ventriculoarterial connection. The common atrioventricular orifice was guarded by an effectively common valve, the right half being guarded by a well-formed three-leaflet valve, but the posterior and left lateral wall of the orifice being deficient of valvar leaflet tissue. The right ventricular inlet was a blind chamber, an imperforate dimple being seen which was surrounded by valvar remnants. The apical trabecular and outlet components of the right ventricle communicated with the left ventricle through an outlet ventricular septal defect in front of the anterosuperior leaflet of the atrioventricular valve, giving the potential clinically for the lesion to be misdiagnosed as double inlet left ventricle.

Original languageEnglish
Pages (from-to)152-154
Number of pages3
JournalCardiology in the Young
Volume1
Issue number2
DOIs
StatePublished - 1 Jan 1991

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Ebstein Anomaly
Heart Ventricles
Isomerism
Atrial Appendage
Ventricular Heart Septal Defects
Diagnostic Errors
Hand
Atrioventricular Septal Defect

Cite this

Seo, Jeong-Wook ; Jung, Woo Hee ; Park, Yong Won. / Imperforate Ebstein's malformation in atrioventricular septal defect. In: Cardiology in the Young. 1991 ; Vol. 1, No. 2. pp. 152-154.
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Imperforate Ebstein's malformation in atrioventricular septal defect. / Seo, Jeong-Wook; Jung, Woo Hee; Park, Yong Won.

In: Cardiology in the Young, Vol. 1, No. 2, 01.01.1991, p. 152-154.

Research output: Contribution to journalArticleResearchpeer-review

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