Chiari 1.5 malformation: An advanced form of chiari I malformation

In Kyeong Kim, Kyuchang Wang, In One Kim, Byung Kyu Cho

Research output: Contribution to journalArticle

20 Citations (Scopus)

Abstract

The Chiari 1.5 malformation is defined as a tonsillar herniation within a Chiari I malformation with additional caudal descent of the brainstem through the foramen magnum. We describe a patient with Chiari I malformation who evolved to Chiari 1.5 malformation during longitudinal follow-up. A 15-year-old girl presented with neck pain during exercise for two years. She had been diagnosed with Chiari I malformation with mild hydrocephalus after minor cervical trauma at the age of six years. At that time, she was asymptomatic. After she complained of aggravated neck pain, neuroimaging (nine years after first imaging) revealed caudal descent of the brainstem and syringomyelia in addition to progression of tonsillar herniation. Posterior fossa decompressive surgery resulted in complete resolution of neck pain. Based on neuroimaging and operative findings, she was diagnosed as Chiari 1.5 malformation. Neuroimaging performed seven months after surgery showed an increased anterior-posterior diameter of the medulla oblongata and markedly decreased syringomyelia. This case demonstrates progressive developmental process of the Chiari 1.5 malformation as an advanced form of the Chiari I malformation.

Original languageEnglish
Pages (from-to)375-379
Number of pages5
JournalJournal of Korean Neurosurgical Society
Volume48
Issue number4
DOIs
StatePublished - 1 Jan 2010

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Neck Pain
Neuroimaging
Encephalocele
Syringomyelia
Brain Stem
Foramen Magnum
Medulla Oblongata
Hydrocephalus
Exercise
Wounds and Injuries

Keywords

  • Chiari 1.5 malformation asymptomatic hydrocephalus syringomyelia

Cite this

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Chiari 1.5 malformation : An advanced form of chiari I malformation. / Kim, In Kyeong; Wang, Kyuchang; Kim, In One; Cho, Byung Kyu.

In: Journal of Korean Neurosurgical Society, Vol. 48, No. 4, 01.01.2010, p. 375-379.

Research output: Contribution to journalArticle

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