A case of embolization seen in pulmonary arteriovenous malformation in a patient with Osler-Rendu-Weber syndrome

Ho Jun Jang, Min Seok Kim, Song Yi Kim, Jung Kyu Han, Yong-Jin Kim, Byung Hee Oh, Hwan Jun Jae

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

Osler-Rendu-Weber Syndrome or hereditary hemorrhagic telangiectasia (HHT) is characterized by telangiectasia of the skin and of the mucous membranes and intermittent bleeding from vascular abnormalities; in about 20% of the patients pulmonary arteriovenous malformation is present. Pulmonary arteriovenous malformation is a congenital anomaly in the lung which causes shunting of venous blood in the pulmonary artery to systemic circulation, resulting in cyanosis, polycythemia and clubbing. Recently we experienced a case of multiple pulmonary arteriovenous malformation associated with the telangiectatic change of the cerebral artery in a 16-year-old male patient, which was confirmed by pulmonary angiography.

Original languageEnglish
Pages (from-to)820-822
Number of pages3
JournalKorean Circulation Journal
Volume36
Issue number12
DOIs
StatePublished - 1 Jan 2006

Fingerprint

Hereditary Hemorrhagic Telangiectasia
Arteriovenous Malformations
Lung
Telangiectasis
Polycythemia
Cyanosis
Cerebral Arteries
Pulmonary Artery
Blood Vessels
Angiography
Mucous Membrane
Hemorrhage
Skin

Keywords

  • Arteriovenous malformation
  • Osler-Rendu-Weber syndrome
  • Telangiectasia, hereditary hemorrhagic

Cite this

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title = "A case of embolization seen in pulmonary arteriovenous malformation in a patient with Osler-Rendu-Weber syndrome",
abstract = "Osler-Rendu-Weber Syndrome or hereditary hemorrhagic telangiectasia (HHT) is characterized by telangiectasia of the skin and of the mucous membranes and intermittent bleeding from vascular abnormalities; in about 20{\%} of the patients pulmonary arteriovenous malformation is present. Pulmonary arteriovenous malformation is a congenital anomaly in the lung which causes shunting of venous blood in the pulmonary artery to systemic circulation, resulting in cyanosis, polycythemia and clubbing. Recently we experienced a case of multiple pulmonary arteriovenous malformation associated with the telangiectatic change of the cerebral artery in a 16-year-old male patient, which was confirmed by pulmonary angiography.",
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author = "Jang, {Ho Jun} and Kim, {Min Seok} and Kim, {Song Yi} and Han, {Jung Kyu} and Yong-Jin Kim and Oh, {Byung Hee} and Jae, {Hwan Jun}",
year = "2006",
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A case of embolization seen in pulmonary arteriovenous malformation in a patient with Osler-Rendu-Weber syndrome. / Jang, Ho Jun; Kim, Min Seok; Kim, Song Yi; Han, Jung Kyu; Kim, Yong-Jin; Oh, Byung Hee; Jae, Hwan Jun.

In: Korean Circulation Journal, Vol. 36, No. 12, 01.01.2006, p. 820-822.

Research output: Contribution to journalArticle

TY - JOUR

T1 - A case of embolization seen in pulmonary arteriovenous malformation in a patient with Osler-Rendu-Weber syndrome

AU - Jang, Ho Jun

AU - Kim, Min Seok

AU - Kim, Song Yi

AU - Han, Jung Kyu

AU - Kim, Yong-Jin

AU - Oh, Byung Hee

AU - Jae, Hwan Jun

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N2 - Osler-Rendu-Weber Syndrome or hereditary hemorrhagic telangiectasia (HHT) is characterized by telangiectasia of the skin and of the mucous membranes and intermittent bleeding from vascular abnormalities; in about 20% of the patients pulmonary arteriovenous malformation is present. Pulmonary arteriovenous malformation is a congenital anomaly in the lung which causes shunting of venous blood in the pulmonary artery to systemic circulation, resulting in cyanosis, polycythemia and clubbing. Recently we experienced a case of multiple pulmonary arteriovenous malformation associated with the telangiectatic change of the cerebral artery in a 16-year-old male patient, which was confirmed by pulmonary angiography.

AB - Osler-Rendu-Weber Syndrome or hereditary hemorrhagic telangiectasia (HHT) is characterized by telangiectasia of the skin and of the mucous membranes and intermittent bleeding from vascular abnormalities; in about 20% of the patients pulmonary arteriovenous malformation is present. Pulmonary arteriovenous malformation is a congenital anomaly in the lung which causes shunting of venous blood in the pulmonary artery to systemic circulation, resulting in cyanosis, polycythemia and clubbing. Recently we experienced a case of multiple pulmonary arteriovenous malformation associated with the telangiectatic change of the cerebral artery in a 16-year-old male patient, which was confirmed by pulmonary angiography.

KW - Arteriovenous malformation

KW - Osler-Rendu-Weber syndrome

KW - Telangiectasia, hereditary hemorrhagic

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